
Dysplastic Cerebellar Epilepsy: Complete Seizure Control Following Resection of a Ganglioglioma
2015; Springer Science+Business Media; Volume: 15; Issue: 4 Linguagem: Inglês
10.1007/s12311-015-0705-5
ISSN1473-4230
AutoresWilliam Alves Martins, Eliseu Paglioli, Marta Hemb, André Palmini,
Tópico(s)Neurological and metabolic disorders
ResumoSubcortical epilepsy has been a controversial issue, partially settled by evidence showing seizure generation in hypothalamic hamartomas and also by reports of seizures caused by cerebellar lesions. We report 4-year-old girl with right hemifacial seizures and autonomic phenomena, in whom MRI showed an irregular mass in the right cerebellar peduncle. Despite several unremarkable video-EEG recordings, seizure origin in the lesion was hypothesized. Complete resection was feasible, histopathology showed a ganglioglioma, and she has been seizure free for 3 years. A fine line separates these developmental tumors from focal cortical dysplasia, and the homogeneous presentation of this entity led us to propose the terminology dysplastic cerebellar epilepsy.
Referência(s)