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Aphallia: Its Classification and Management

1989; Lippincott Williams & Wilkins; Volume: 141; Issue: 3 Part 1 Linguagem: Inglês

10.1016/s0022-5347(17)40903-7

1527-3792

Steven J. Skoog, A. Barry Belman,

Urologic and reproductive health conditions

No AccessJournal of Urology1 Mar 1989Aphallia: Its Classification and Management Steven J. Skoog, and A. Barry Belman Steven J. SkoogSteven J. Skoog , and A. Barry BelmanA. Barry Belman View All Author Informationhttps://doi.org/10.1016/S0022-5347(17)40903-7AboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissionsReprints ShareFacebookLinked InTwitterEmail Aphallia is an extremely rare disorder with profound urological and psychological consequences. Approximately 60 patients have been reported on in the literature; we report our experience with 3 additional patients. Fifty patients had sufficient information to classify the condition according to the site of the urethral meatus. With the relative relationship of the urethral meatus to the anal sphincter several observations were noted. The more proximal the meatus the higher the incidence of other anomalies and the greater the number of neonatal deaths. Of the patients 30 (60 per cent) had a post-sphincteric meatus located on a peculiar appendage at the anal verge. These patients had the lowest incidence of other anomalies (1.2 per patient) and the highest survival rate (87 per cent). A total of 14 patients (28 per cent) had pre-sphincteric urethral communications (prostatorectal fistula), of whom 36 per cent died in the neonatal period. Six patients (12 per cent) had urethral atresia. This group had no survivors and the highest incidence of other anomalies (4 per patient). Of our patients 2 had a post-sphincteric meatus and 1 had a pre-sphincteric meatus. In addition to correction of life-threatening anomalies the management of aphallia centers on establishing gender assignment. Bilateral orchiectomy, labial construction and urethral transposition should be done in the newborn period, if possible. © 1989 by The American Urological Association Education and Research, Inc.FiguresReferencesRelatedDetailsCited ByDe Castro R, Merlini E, Rigamonti W and Macedo A (2018) Phalloplasty and Urethroplasty in Children With Penile Agenesis: Preliminary ReportJournal of Urology, VOL. 177, NO. 3, (1112-1117), Online publication date: 1-Mar-2007.YOO J, LEE I and ATALA A (2018) CARTILAGE RODS AS A POTENTIAL MATERIAL FOR PENILE RECONSTRUCTIONJournal of Urology, VOL. 160, NO. 3 Part 2, (1164-1168), Online publication date: 1-Sep-1998.Kaefer M and Adams M (2018) Penis and Bladder Agenesis in a Living Male NeonateJournal of Urology, VOL. 157, NO. 4, (1439-1440), Online publication date: 1-Apr-1997.Hendren W (2018) The Genetic Male With Absent Penis and Urethrorectal Communication: Experience With 5 PatientsJournal of Urology, VOL. 157, NO. 4, (1469-1474), Online publication date: 1-Apr-1997.Gilbert J, Clark R and Koyle M (2018) Penile Agenesis: A Fatal Variation of an Uncommon LesionJournal of Urology, VOL. 143, NO. 2, (338-339), Online publication date: 1-Feb-1990. Volume 141Issue 3 Part 1March 1989Page: 589-592 Advertisement Copyright & Permissions© 1989 by The American Urological Association Education and Research, Inc.MetricsAuthor Information Steven J. Skoog More articles by this author A. Barry Belman More articles by this author Expand All Advertisement Loading ...