Bilateral Testicular Adrenal Rests in a Patient with 11-Hydroxylase Deficient Congenital Adrenal Hyperplasia
1993; Lippincott Williams & Wilkins; Volume: 149; Issue: 2 Linguagem: Inglês
10.1016/s0022-5347(17)36079-2
ISSN1527-3792
AutoresAmitai Oberman, E Flatau, Rafael Luboshitzky,
Tópico(s)Metabolism and Genetic Disorders
ResumoNo AccessJournal of UrologyPediatric Articles1 Feb 1993Bilateral Testicular Adrenal Rests in a Patient with 11-Hydroxylase Deficient Congenital Adrenal Hyperplasia Amitai S. Oberman, Edith Flatau, and Rafael Luboshitzky Amitai S. ObermanAmitai S. Oberman More articles by this author , Edith FlatauEdith Flatau More articles by this author , and Rafael LuboshitzkyRafael Luboshitzky More articles by this author View All Author Informationhttps://doi.org/10.1016/S0022-5347(17)36079-2AboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissionsReprints ShareFacebookLinked InTwitterEmail A 13-year-old boy was referred for investigation of hypertension, precocious puberty and giant testicles. Hormonal studies established the diagnosis of congenital adrenal hyperplasia due to 11-hydroxylase deficiency. Testicular biopsy revealed that the scrotal masses were adrenal rest tumors entirely composed of adrenocortical tissue. Primary testicular tissue was absent. The size of the tumors regressed following replacement steroid therapy together with restoration of normal blood pressure. This observation of a testicular adrenal rest tumor in a patient with 11-hydroxylase deficient congenital adrenal hyperplasia is unique. © 1993 by The American Urological Association Education and Research, Inc.FiguresReferencesRelatedDetailsCited byRUBENSTEIN R, DOGRA V, SEFTEL A and RESNICK M (2018) Benign Intrascrotal LesionsJournal of Urology, VOL. 171, NO. 5, (1765-1772), Online publication date: 1-May-2004.Walker B, Skoog S, Winslow B, Canning D and Tank E (2018) Testis Sparing Surgery for Steroid Unresponsive Testicular Tumors of the Adrenogenital SyndromeJournal of Urology, VOL. 157, NO. 4, (1460-1463), Online publication date: 1-Apr-1997. Volume 149Issue 2February 1993Page: 350-352 Advertisement Copyright & Permissions© 1993 by The American Urological Association Education and Research, Inc.Keywordstesticular neoplasmscongenitalhydroxylasesadrenal rest tumoradrenal hyperplasiaMetricsAuthor Information Amitai S. Oberman More articles by this author Edith Flatau More articles by this author Rafael Luboshitzky More articles by this author Expand All Advertisement PDF downloadLoading ...
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