Proximal-type epithelioid sarcoma—unusual presentation: unilateral vulvar mass
2015; BMJ; Linguagem: Inglês
10.1136/bcr-2014-208488
ISSN1757-790X
AutoresAna Isabel Rodrigues, Helena Isabel Lopes, Olinda Lima, Susana Marta,
Tópico(s)Cardiac tumors and thrombi
ResumoEpithelioid sarcoma of the vulva is a very rare malignant soft tissue tumour, usually initially asymptomatic, which simulates a variety of benign lesions, leading to diagnosis only at later stages. Prognosis is generally poor. We report a case of a 55-year-old postmenopausal woman, who presented with rapid growth of an asymptomatic mass located in the left labia majora. Biopsy of the lesion revealed features characteristic of proximal-type epithelioid sarcoma. Ganglionar, adrenal, pulmonary and hepatic metastases were found at thoracoabdominopelvic CT scan. During hospitalisation, the patient’s clinical condition suffered rapid deterioration and she died on the 16th day of admission.
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