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Aneurisma aórtico en el síndrome de Alagille

2008; Elsevier BV; Volume: 61; Issue: 6 Linguagem: Inglês

10.1157/13123079

1579-2242

Edmundo Molinero-Herguedas, Tomás Labrador-Fuster, Miguel Ríos-Lázaro, Jorge Carmaniú-Tobal,

Congenital Anomalies and Fetal Surgery

Alagille syndrome affects multiple organ systems. The most common vascular manifestation of Alagille syndrome is peripheral pulmonary artery stenosis. A few cases of abdominal vasculature involvement have been reported, particularly in the pediatric age group. Herein, the authors describe an adult patient with Alagille syndrome who presented with multiple visceral vascular abnormalities, including a high-grade stenosis of the celiac artery, superior mesenteric artery (SMA), aneurysms of the distal common hepatic artery, and distal SMA detected with computed tomographic angiography.