Supraventricular tachycardia in a patient with Lown-Ganong-Levine syndrome associated with apical hypertrophic cardiomyopathy.
1988; Japanese Heart Journal Assoc; Volume: 29; Issue: 2 Linguagem: Inglês
10.1536/ihj.29.249
ISSN1573-8612
AutoresMotonobu Hayano, Yoichi Imamura, Mitsuhiro Tsuruta, Junichi Inoue, Hiroshi Nakashima, Kuniaki FUKUYAMA, Yoshiki Eguchi, Shinsuke Tsuji, Shuzo Matsuo, Katsusuke Yano,
Tópico(s)Cardiac Structural Anomalies and Repair
ResumoElectrophysiologic study of a 55-year-old patient with Lown-Ganong-Levine syndrome associated with apical hypertrophic cardiomyopathy is reported. The patient had a history of recurrent attacks of tachyarrhythmia and his electrocardiogram showed a short P-R interval (0.10 see) with narrow QRS complex and left ventricular hypertrophy with giant negative T waves. His cineangiogram showed severe apical hypertrophy. An electrophysiologic study was performed. The results of programmed atrial pacing show the existence of the dual A-V nodal pathways. The A-H interval at rapid atrial pacing increased maximally by 103 msec. Atrial stimulation could depolarize parts of the atrium without altering the supraventricular tachycardia. These findings suggested that preferential rapidly conducting A-V nodal and intranodal reentry are the responsible mechanisms in this reciprocating tachycardia.We conclude that the short P-R interval was due to intranodal reentry through the dual A-V nodal pathways. To our knowledge, a case of Lown-Ganong-Levine syndrome with apical hypertrophic cardiomyopathy has not been previously described in the literature.
Referência(s)