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Atrial septal defect associated with mitral stenosis

1970; Elsevier BV; Volume: 48; Issue: 3 Linguagem: Inglês

10.1016/0002-9343(70)90059-8

1555-7162

W Steinbrunn, Keith Cohn, Arthur Selzer,

Congenital Heart Disease Studies

Five patients are described with large, congenital secundum atrial septal defects combined with acquired rheumatic mitral stenosis. In one additional patient mitral stenosis was associated with a small patency of the foramen ovale, perhaps secondary to atrial wall stretching. Clinically, these cases of Lutembacher's syndrome may resemble pure mitral stenosis in some instances and pure atrial septal defect in others. The dangers of incomplete diagnosis and surgery are emphasized: Increased pressure developing in the left atrium after closure of the atrial defect resulted in pulmonary edema and death in one case and in reopening of the atrial septal defect in two others. Although not a particularly distinctive syndrome, distinguishing features of both conditions are usually present and may permit establishment of the correct diagnosis.