Three Choroid Plexus Papillomas in a Patient with Aicardi Syndrome
2000; Karger Publishers; Volume: 33; Issue: 4 Linguagem: Inglês
10.1159/000055956
ISSN1423-0305
AutoresDerek A. Taggard, Arnold H. Menezes,
Tópico(s)Cerebrospinal fluid and hydrocephalus
ResumoAicardi syndrome is an X-linked dominant disorder primarily defined by the triad of corpus callosum agenesis, infantile spasms and a pathognomonic lacunar chorioretinopathy. Papillomas of the choroid plexus have been reported in affected patients. We report an Aicardi syndrome patient who had three separate choroid plexus papillomas and associated hydrocephalus. A dizygotic twin was unaffected. Staged resection of the tumors was safely accomplished, with improvement in seizure control. Imaging between procedures revealed rapid tumor growth.
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