Cardiovascular disease of connective tissue origin
1987; Elsevier BV; Volume: 82; Issue: 3 Linguagem: Inglês
10.1016/0002-9343(87)90448-7
ISSN1555-7162
AutoresJuan Bowen, Harisios Boudoulas, Charles F. Wooley,
Tópico(s)Urological Disorders and Treatments
ResumoInherited abnormalities of connective tissue elements often cause changes in the structure and function of the cardiovascular system. Well-known heritable disorders of connective tissue in which cardiovascular abnormalities are prominent include the Marfan syndrome and the Ehlers-Danlos syndrome. Connective tissue abnormalities also occur without the associated features of a recognized syndrome. These include isolated valvular prolapse and anuloaortic ectasia. In this review, the cardiovascular features of connective tissue abnormalities—both the recognized syndromes and the isolated abnormalities—are described, important concepts in the diagnosis and treatment of these disorders are reviewed, and the classification of inherited connective tissue abnormalities of the cardiovascular system is discussed.
Referência(s)