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Metastatic Hepatic Epithelioid Hemangioendothelioma in a Teenage Girl

2008; Lippincott Williams & Wilkins; Volume: 30; Issue: 7 Linguagem: Inglês

10.1097/mph.0b013e31816e22d1

1536-3678

Alisha Kassam, Karen Mandel,

Eosinophilic Disorders and Syndromes

Hepatic epithelioid hemangioendothelioma (HEHE) is a rare malignant tumor characterized by its epithelioid structure and vascular endothelium origin. The clinical course of HEHE is variable, ranging from long-term survival without treatment to a rapidly progressive course with a fatal outcome. As a consequence, no standard treatment has been determined. We present a case of HEHE occurring in a 13-year-old girl, in which a novel treatment approach using antiangiogenic therapy was tried and was successful in slowing the progression of the disease.