Portal de Periódicos da CAPES

Alstrom syndrome: A case report.

2001; Nihon University; Volume: 43; Issue: 3 Linguagem: Inglês

10.2334/josnusd.43.221

1880-4926

Fatma Koray, Can Dörter, Yasemin Benderli, İlhan Satman, Temel Yılmaz, Nevin Dınççağ, Kubilay Karşıdağ,

Bone and Dental Protein Studies

Alstrom syndrome is a rare disorder characterized by early obesity, loss of central vision, diabetes mellitus, hearing loss and short stature. Previous studies, have reported no information regarding oral findings. This article describes oral findings in two cases of Alstrom syndrome. In both cases, gingivitis was present and also light yellowbrown discolored enamel bands were observed on the anterior teeth. This staining may have resulted from discoloration of the preexisting slight band-like enamel hypoplasia. The gingiva was examined histologically by light and transmission electron microscopy. Irregular thickness of the basal lamina and delamination of the myelin sheath were detected by transmission electron microscopy. There is no information about pathological odontogenesis in Alstrom syndrome in previous reports. Oral present findings may contribute further information about the clinical manifestations of Alstrom syndrome. (J. Oral Sci. 43, 221-224, 2001)