Artigo Acesso aberto Produção Nacional Revisado por pares

Supravalvular Congenital Mitral Stenosis

2002; Sociedade Brasileira de Cardiologia (SBC); Volume: 79; Issue: 1 Linguagem: Inglês

10.1590/s0066-782x2002001000008

ISSN

1678-4170

Autores

Fernando Moraes, Cleuza Lapa, Cristina Ventura, Rejane Conceição Santana, Euclides Tenório, Cláudio A Gomes, Carlos R. Moraes,

Tópico(s)

Congenital Heart Disease Studies

Resumo

Congenital supravalvular mitral stenosis is a rare malformation characterized by the presence of a shelf-like fibrous membrane, with 1 or 2 small orifices, covering and obstructing the mitral valve. The membrane is positioned closely to the mitral valve (and sometimes it is attached to it); therefore, a preoperative diagnosis is inevitably difficult, even with the use of biplane echocardiography. Two patients with supravalvular mitral stenosis aged 3 years and 3 months are described. In 1 patient, a preoperative diagnosis was made, and both successfully underwent correction.

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