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Management of Epidermolysis Bullosa Acquisita

2011; Elsevier BV; Volume: 29; Issue: 4 Linguagem: Inglês

10.1016/j.det.2011.06.020

1558-0520

Lizbeth R.A. Intong, Dédée F. Murrell,

Coagulation, Bradykinin, Polyphosphates, and Angioedema

Epidermolysis bullosa acquisita is a rare and debilitating autoimmune mucocutaneous blistering disease caused by autoantibodies directed against type VII collagen or anchoring fibrils in the subepidermal basement membrane zone . Treatment is quite challenging because this disease can be recalcitrant to multiple modalities. This article discusses the current management of this disease.