Aplasia Cutis Congenita and Arteriovenous Fistula

1990; American Medical Association; Volume: 47; Issue: 11 Linguagem: Inglês

10.1001/archneur.1990.00530110117028

ISSN

1538-3687

Autores

Romaine Singman,

Tópico(s)

Congenital limb and hand anomalies

Resumo

We describe a child with congenital aplasia cutis congenita of the scalp and an occult giant posterior fossa arteriovenous fistula. Previous case reports of central nervous system malformations associated with aplasia cutis congenita are reviewed. The exact incidence of such malformations is unknown. All patients with aplasia cutis congenita should undergo a neurologic evaluation, and their families should be examined for similar lesions. Early central nervous system imaging and other workup may be required, especially if plastic surgery in the head region is being planned.

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