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Lupus erythematosus tumidus in Childhood

2003; Karger Publishers; Volume: 207; Issue: 2 Linguagem: Inglês

10.1159/000071793

1421-9832

Monika Sonntag, Percy Lehmann, Mosaad Megahed, Thomas Ruzicka, Annegret Kuhn,

Autoimmune Bullous Skin Diseases

Lupus erythematosus (LE) is a rare disorder in childhood. Most patients reported in the literature present with systemic manifestations, and, to date, fewer than 20 children with chronic cutaneous LE have been documented. In this article, we describe 3 patients with childhood LE tumidus, an uncommon but distinct subtype of chronic cutaneous LE. The lesions are characterized by erythematous, urticaria-like, nonscarring plaques in sun-exposed areas and, unlike in other variants of chronic cutaneous LE, there is no epidermal involvement. The clinical, photobiological, and histologic features as well as the differential diagnoses of childhood LE tumidus are discussed and compared with the adult form of this disease.