Artigo Revisado por pares

Dihydroxyadenine Urolithiasis in Children with Partial Deficiency of Adenine Phosphoribosyltransferase

1981; Karger Publishers; Volume: 36; Issue: 4 Linguagem: Inglês

10.1159/000280771

ISSN

1423-0399

Autores

Kimitaka Sakamoto, Yasuhito Fujisawa, Akio Ohmori, Kaoru Minoda, Hisashi Yamanaka, Kusuki Nishioka,

Tópico(s)

Adolescent and Pediatric Healthcare

Resumo

Urolithiasis composed of 2,8-dihydroxyadenine is not only formed in a complete defect of adenine phosphoribosyltransferase, but also in a partial deficiency of this enzyme. To our knowledge these cases reported in this paper are the third and fourth cases of dihydroxyadenine urinary calculi in patients with partial deficiency of adenine phosphoribosyltransferase.

Referência(s)