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Hepatectomía derecha extendida por colangiocarcinoma intrahepático en un paciente con síndrome de Dubin-Johnson

2009; Elsevier BV; Volume: 61; Issue: 3 Linguagem: Inglês

10.4067/s0718-40262009000300011

0718-4026

CRISTIAN GAMBOA C, RICARDO YÁÑEZ M, Jorge Martínez C, Marco Arrese J, Bruno Nervi N, YERKO BORGHERO E, Javiera Torres M, Nicolás Jarufe C,

Metabolism and Genetic Disorders

Hepatectomy for cholangiocarcinoma in one patient with Dubin Johnson syndromeDubin-Johnson syndrome (SDJ) is a rare benign autosomal recessive congenital disease that causes jaundice.We report a 71 years old male with a Dubin Jonson syndrome diagnosed at the age of 40.On a ultrasound examination and magnetic resonance imaging, a liver tumor was found, that was excised.The pathology report showed a cholangiocarcinoma.During the postoperative period, the patient had a hyperbilirubinemia that subsided slowly.There are reports of hyperbilirubinemia of difficult management after hepatectomy in patients with Dubin-Johnson syndrome.