Adult Diagnosis of Swyer-James-Macleod Syndrome: Retrospective Analysis of Four Cases
2013; American Association for Respiratory Care; Volume: 59; Issue: 4 Linguagem: Inglês
10.4187/respcare.02552
ISSN1943-3654
AutoresHadice Selimoğlu Şen, Mahşuk Taylan, Özlem Abakay, Cengizhan Sezgı, Mehmet Güli Çetinçakmak,
Tópico(s)Tracheal and airway disorders
ResumoSwyer-James-Macleod syndrome (SJMS) is a rare constrictive bronchiolitis with air-flow obstruction and a decreased number and diameter of ipsilateral peripheral pulmonary vessels. This syndrome is characterized by unilateral hyperlucency on chest radiography. Computed tomography provides useful additional information. The diagnosis is usually made in childhood but sometimes occurs in adulthood. The disease often presents with dyspnea, decreased exercise tolerance, cough, hemoptysis, and recurrent pulmonary infections. SJMS may be confused with asthma or pulmonary embolism due to similar symptoms and may result in inappropriate therapy. This case series examined the clinical and imaging spectrum of four patients who were diagnosed with SJMS in adulthood.
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