Portal de Periódicos da CAPES

Arteriovenous shunting as a new feature of PHACES

2009; Volume: 3; Issue: 1 Linguagem: Inglês

10.3171/2008.10.peds08169

1933-0715

Huan Wang, Albert K. Oh, Darren B. Orbach,

Retinal and Macular Surgery

Patients with the congenital neurocutaneous disorder PHACES are at a markedly increased risk of ischemic infarction during childhood. Although intracranial arterial anomalies have been well described, venous abnormalities have not been documented. The authors report on a unique case of a 3-month-old girl with PHACES and a skull base osteodural arteriovenous fistula. A separate arteriovenous shunt at T-5 may also have been present. Imaging findings and treatment strategies are discussed.