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Fronto-Temporal Dementia and Motor Neuron Disease: a neuropsychological study

2009; Wiley; Volume: 100; Issue: 5 Linguagem: Inglês

10.1111/j.1600-0404.1999.tb00408.x

1600-0404

Valentina Gentileschi, Silvia Muggia, M. Poloni, Hans Spinnler,

Parkinson's Disease Mechanisms and Treatments

Acta Neurologica ScandinavicaVolume 100, Issue 5 p. 341-349 Fronto-Temporal Dementia and Motor Neuron Disease: a neuropsychological study V. Gentileschi, V. Gentileschi Third Neurological Department of the University of MilanSearch for more papers by this authorS. Muggia, S. Muggia Third Neurological Department of the University of MilanSearch for more papers by this authorM. Poloni, M. Poloni Third Neurological Department of the University of MilanSearch for more papers by this authorH. Spinnler, Corresponding Author H. Spinnler Third Neurological Department of the University of Milan Following our normal practice, names are listed in alphabetical order, and this does not imply differential contribution to the paper.Hans Spinnler, Clinica Neurologica II dell'Università di Milano, Dipartimento di Medicina, Chirurgia ed Odontoiatria, Polo Didattico San Paolo, Via Antonio Starabba di Rudini, 8-20142 Milano, ItalySearch for more papers by this author V. Gentileschi, V. Gentileschi Third Neurological Department of the University of MilanSearch for more papers by this authorS. Muggia, S. Muggia Third Neurological Department of the University of MilanSearch for more papers by this authorM. Poloni, M. Poloni Third Neurological Department of the University of MilanSearch for more papers by this authorH. Spinnler, Corresponding Author H. Spinnler Third Neurological Department of the University of Milan Following our normal practice, names are listed in alphabetical order, and this does not imply differential contribution to the paper.Hans Spinnler, Clinica Neurologica II dell'Università di Milano, Dipartimento di Medicina, Chirurgia ed Odontoiatria, Polo Didattico San Paolo, Via Antonio Starabba di Rudini, 8-20142 Milano, ItalySearch for more papers by this author First published: 29 January 2009 https://doi.org/10.1111/j.1600-0404.1999.tb00408.xCitations: 5 AboutPDF ToolsRequest permissionExport citationAdd to favoritesTrack citation ShareShare Give accessShare full text accessShare full-text accessPlease review our Terms and Conditions of Use and check box below to share full-text version of article.I have read and accept the Wiley Online Library Terms and Conditions of UseShareable LinkUse the link below to share a full-text version of this article with your friends and colleagues. Learn more.Copy URL Share a linkShare onFacebookTwitterLinked InRedditWechat Abstract The neuropsychological follow-up study of a 58-year-old man suffering from Motor Neuron Disease (ALS/MND) and Fronto-Temporal Dementia (FTD) is reported. Neuromuscular signs first appeared at the age of 51 and slowly progressed to late bulbar involvement; behavioural symptoms of the frontal type first appeared around age 53; lastly, several neuropsychological symptoms suggestive of worsening temporal involvement supervened at age 57. Our patient died at 59 of respiratory failure with the classic clinical and neuroradiological picture of FTD. A short discussion addresses the controversial issue of the coupling of ALS/MND with Dementia and its possible interpretation as the expression of a chance association of relatively common diseases, versus that of a single multifaceted disease. The role of a detailed neuropsychological assessment is highlighted, within the context of increasingly specific diagnostic criteria for FTD. Citing Literature Volume100, Issue5November 1999Pages 341-349 RelatedInformation