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SENSORINEURAL HEARING LOSS AND CONGENITAL HETEROCHROMIA IRIDIUM

1969; American Medical Association; Volume: 117; Issue: 3 Linguagem: Inglês

10.1001/archpedi.1969.02100030373027

1538-3628

Robert J. Gorlin,

Congenital Ear and Nasal Anomalies

To The Editor .—I was extremely interested in the perspicacious report of Dr. G. C. Robinson and Dr. V. J. Wright on Sensorineural Hearing Loss and Congenital Heterochromia Iridium (Amer J Dis Child 116: 106-109 [July] 1968). Dr. Robinson and colleagues have been very seminal contributors, and their acute observations have been of keen interest to this reader. Although, as an oral pathologist I have no direct involvement with this syndrome, nevertheless, syndromes of profound childhood deafness have captured my interest, and I have catalogued over 50 such symptom-complexes. Dr. Robinson and Dr. Wright indicated in their report that this binary complex with auricular appendages had not been previously reported. It would appear, however, that the report by McLaurin et al, Hereditary Branchial Anomalies and Associated Hearing Impairment ( Laryngoscope 76 : 1277-1288 [July] 1966), may well illustrate this syndrome. The association of hereditary deafness (autosomal dominant) with pretragal ear pits and