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Impaired Neutrophil Kinesis in a Patient with the Shwachman-Diamond Syndrome

1978; Wiley; Volume: 14; Issue: 1 Linguagem: Inglês

10.1111/j.1440-1754.1978.tb02936.x

1440-1754

Y.H. Thong,

Infective Endocarditis Diagnosis and Management

Journal of Paediatrics and Child HealthVolume 14, Issue 1 p. 34-37 Impaired Neutrophil Kinesis in a Patient with the Shwachman-Diamond Syndrome Y. H. THONG, Corresponding Author Y. H. THONG Department of Paediatrics, University of Adelaide, The Adelaide Children's Hospital, North Adelaide, 5006, South AustraliaDepartment of Paediatrics, The Adelaide Children's Hospital, North Adelaide, 5006, South Australia.Search for more papers by this author Y. H. THONG, Corresponding Author Y. H. THONG Department of Paediatrics, University of Adelaide, The Adelaide Children's Hospital, North Adelaide, 5006, South AustraliaDepartment of Paediatrics, The Adelaide Children's Hospital, North Adelaide, 5006, South Australia.Search for more papers by this author First published: March 1978 https://doi.org/10.1111/j.1440-1754.1978.tb02936.xAboutPDF ToolsRequest permissionExport citationAdd to favoritesTrack citation ShareShare Give accessShare full text accessShare full-text accessPlease review our Terms and Conditions of Use and check box below to share full-text version of article.I have read and accept the Wiley Online Library Terms and Conditions of UseShareable LinkUse the link below to share a full-text version of this article with your friends and colleagues. Learn more.Copy URL Share a linkShare onEmailFacebookTwitterLinkedInRedditWechat Abstract Impaired neutrophil kinesis in a patient with the Shwachman-Diamond syndrome. Recurrent infections contribute significantly to morbidity and mortality in the Shwachman-Diamond syndrome. There is no correlation between infectious episodes and degree of duration of neutropenia. The finding of a chemotactic disorder in a patient with this syndrome may explain, in part, the susceptibility of these patients to infection. REFERENCES Bellanti, J. A., and Dayton, D. H. (1975), The phagocytic cell in host resistance, New York , Raven Press. Google Scholar Brueton, M. J., Mavromichalis, J., Goodchild, M. C., and Anderson, C. M. (1977), Hepatic dysfunction in association with pancreatic insufficiency and cyclical neutropaenia, Arch. Dis. Child., 52: 76–78. 10.1136/adc.52.1.76 CASPubMedWeb of Science®Google Scholar Dienard, A. S., Fortuny, I. F., Theologides, A., Anderson, G. L., Boen, J., and Kennedy, B. J. (1974), Studies on the neutropenia of cancer chemotherapy. 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