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On the mechanism of sudden death in Moersch‐Woltman syndrome

1983; Lippincott Williams & Wilkins; Volume: 33; Issue: 7 Linguagem: Inglês

10.1212/wnl.33.7.930

1526-632X

Christopher G. Goetz, Harold L. Klawans,

Glycogen Storage Diseases and Myoclonus

A patient dying in the hospital with Moersch-Woltman Stiff-person syndrome (MWS) suffered from episodic, severe, uncompensated metabolic acidosis. Possible explanations for the acid-base abnormalities in this neurologic disorder are proposed.