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Partial splenectomy in cystic fibrosis patients with hypersplenism

2003; BMJ; Volume: 88; Issue: 2 Linguagem: Inglês

10.1136/adc.88.2.143

1468-2044

G. Thalhammer,

Genetic and Kidney Cyst Diseases

We report three cystic fibrosis (CF) patients with hypersplenism who underwent partial splenectomy. The postoperative course was uneventful in two patients; one patient developed a complication necessitating resection of the rest of the spleen. Haematological parameters improved and oesophageal varices regressed in all patients. On follow up, one patient showed a normal spleen, the other a normally functioning accessory spleen; the third patient again developed splenomegaly with hypersplenism. Partial splenectomy is a promising therapeutic option for CF patients with hypersplenism.