Portal de Periódicos da CAPES

Successful Tacrolimus Therapy Extended by Everolimus in Retroperitoneal Angiomyolipoma after Lung Transplantation: A Case Report

2014; Scientific Research Publishing; Volume: 03; Issue: 12 Linguagem: Inglês

10.4236/crcm.2014.312135

2325-7075

Tamás Erdélyi, Anikó Bohács, Krisztina Vincze, Zsuzsanna Kováts, Veronika Sárosi, András Sinkovicz, György Balázs, Veronika Müller,

Eosinophilic Disorders and Syndromes

Lymphangioleiomyomatosis (LAM) is a rare disease that affects women, especially in child-bearing age. Clinical manifestations include angiomyolipoma, pneumothorax, chylothorax, cystic changes of lungs and progressive pulmonary failure. In this article, we report a case of lung transplantation (LuTX) for end stage pulmonary LAM and the treatment of angiomyolipoma showing growth after LuTX resulting in complete remission with combination therapy of everolimus and tacrolimus.