Portal de Periódicos da CAPES

Mutilating palmoplantar keratoderma with periorificial keratotic plaques (Olmsted's syndrome)

1990; Oxford University Press; Volume: 122; Issue: 2 Linguagem: Inglês

10.1111/j.1365-2133.1990.tb08271.x

1365-2133

David J. Atherton, CAROLINE SUTTON, Bradley Jones,

Dermatologic Treatments and Research

We report the case of a boy, now aged 4 years, with a progressive, painful and disabling palmoplantar keratoderma, associated with well-defined hyperkeratotic plaques around the mouth and nostrils. His mother has an identical palmoplantar keratoderma. The palmoplantar keratoderma failed to improve with etretinate, but considerable benefit resulted from full-thickness excision of the skin of both palms, followed by skin grafting. We believe that he has a distinctive but extremely rare form of hereditary palmoplantar keratoderma, first described by Olmsted.