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Hypogenetic lung syndrome in an adolescent: Imaging findings with short review

2008; Medknow; Volume: 3; Issue: 2 Linguagem: Inglês

10.4103/1817-1737.39639

1817-1737

MohamedFiroze Ahamed, Fahad Al-Hameed,

Congenital Heart Disease Studies

Hypogenetic lung syndrome is more popularly known as a scimitar syndrome (SS). It is a rare developmental lung malformation which almost always occurs on the right side. The two most constant features of this syndrome are anomalous pulmonary venous return into systemic circulation, most frequently via inferior vena cava (IVC), and lung hypoplasia.We are reporting such a case illustrating most typical and some uncommon features on chest radiograph and multislice computer tomography (MSCT) of chest. Focal herniation of liver through a diaphragmatic defect presenting as an ovoid soft tissue mass in right lower paraspinal region on chest X ray mimicking sequestration is an interesting but rare finding.