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Recurrent Pulmonary Capillary Hemangiomatosis After Bilateral Lung Transplantation

2010; Lippincott Williams & Wilkins; Volume: 25; Issue: 3 Linguagem: Inglês

10.1097/rti.0b013e3181adebc7

1536-0237

Christopher Lee, Robert D. Suh, Mayil S. Krishnam, Chi Lai, Michael C. Fishbein, W. Dean Wallace, Alice Chen, Rajeev Saggar, Rajan Saggar, John A. Belperio, A. Ardehali, David J. Ross,

Vascular Anomalies and Treatments

Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary hypertension characterized by uncontrolled capillary proliferation in the pulmonary interstitium and alveolar walls. Lung transplantation remains the only definitive treatment. To date, there have been no reported cases of recurrent PCH after lung transplantation. We present a case that describes important radiologic and clinical features of PCH and raises questions about its pathogenesis.