Frantz's tumor: Is mutilating surgery always justified in young patients?
2010; Elsevier BV; Volume: 20; Issue: 2 Linguagem: Inglês
10.1016/j.suronc.2009.12.003
ISSN1879-3320
AutoresManuela Campanile, Avellaneda Nicolás, Stéfane Lebel, A. Delarue, J.M. Guys, Pascal de Lagausie,
Tópico(s)Cholangiocarcinoma and Gallbladder Cancer Studies
ResumoSolid pseudopapillary tumor (Frantz's tumor) of the pancreas is a rare lesion. It is of low-grade malignancy but can cause extensive local invasion. The aim of this study was to assess the outcome of Frantz's tumors after incomplete resection.We contacted all authors who published case reports describing incomplete resection of Frantz's tumor between 1985 and 2008 to request follow-up information.Follow-up information was obtained for 11 out 18 patients who underwent incomplete resection. Estimated median survival rate was 5.7 years (69.5 months).Since Frantz's tumor typically develops mainly in children and young women, a 5.7 year survival rate is unacceptable. Thus complete resection of locally invasive solid-pseudopapillary tumor of the pancreas is always justified, even at the price of difficult, mutilating surgery.
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