Desmoplastic fibroma of bone
1991; Wiley; Volume: 68; Issue: 9 Linguagem: Inglês
10.1002/1097-0142(19911101)68
ISSN1097-0142
AutoresCarrie Y. Inwards, K. Krishnan Unni, John W. Beabout, Franklin H. Sim,
Tópico(s)Sarcoma Diagnosis and Treatment
ResumoDesmoplastic fibroma is a rare primary tumor of bone that histologically and biologically mimics the extra-abdominal desmoid tumor of soft tissue. This study reviews 27 cases of desmoplastic fibroma, consisting of 9 from the Mayo Clinic files and 18 from our consultation files. There was a male predominance, and 74% of the patients were in the first 3 decades of life. The most frequent sites of involvement were the metaphysis of long bones and the mandible. Radiographically, the tumors were lucent, expansile lesions with well-defined margins. Histologically, they contained slender spindle cells and various amounts of collagen fibers. En bloc resection is the treatment of choice because a high incidence of recurrence was noticed after lesional curettage.
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