Artigo Revisado por pares

Bilateral orbital involvement in Erdheim-Chester disease

1998; Taylor & Francis; Volume: 17; Issue: 2 Linguagem: Inglês

10.1076/orbi.17.2.97.2758

ISSN

1744-5108

Autores

P. De Palma, L. Ravalli, Filippo Grisanti, Antônio Rossi, Andrea Marzola, Ingrid Nielsen,

Tópico(s)

Myeloproliferative Neoplasms: Diagnosis and Treatment

Resumo

Erdheim-Chester disease is an idiopathic condition characterized by a xanthogranulomatous process infiltrating the bones, lungs, heart, retroperitoneum and other tissues. This condition is often fatal. Ocular findings are rare. The authors report a case of bilateral xanthelasmas and bilateral massive orbital infiltration in a 61-year-old man with severe retroperitoneal fibrosis, renal and cardiovascular problems. The ophthalmic manifestations and differential diagnosis of this peculiar pathologic condition are discussed.

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