Management of the hemophilic pseudotumor of the abdomen: A rare pathological entity
2014; Elsevier BV; Volume: 5; Issue: 11 Linguagem: Inglês
10.1016/j.ijscr.2014.08.022
ISSN2210-2612
AutoresJavier López-Gómez, Juan S. Contreras, Marco Figueroa-Ruiz, Erick Servín-Torres, José Arturo Velázquez-García, Francisco Bevia-Pérez, Germán Delgadillo-Teyer,
Tópico(s)Coagulation, Bradykinin, Polyphosphates, and Angioedema
ResumoHemophilic pseudotumor is a rare complication that occurs in patients with severe hemophilia. Results from multiple episodes of bleeding into the bones and soft tissues.A 31 years old male patient, with severe hemophilia A. Diagnosed with an abdominal tumor 10 years ago during routine screening, that progressively grew to encompass the entire abdominal area, with symptoms of intestinal obstruction.Hemophilic pseudotumor appears as a painless tumor of slow growth that can compress vital organs producing bone destruction, muscle and skin necrosis. The tumor may have fistulas or break spontaneously.The abdominal hemophilic pseudotumor is a rare pathological entity, with few reports worldwide, but must be considered in hemophilic patients with a well documented abdominal tumor.
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