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Scimitar etcetera — the dysmorphic right lung

1988; Elsevier BV; Volume: 39; Issue: 1 Linguagem: Inglês

10.1016/s0009-9260(88)80329-5

1365-229X

Jason Partridge, Jonathan Osborne, R. Slaughter,

Neonatal Respiratory Health Research

‘Dysmorphic lung’ is introduced as a term to describe any complex congenital malformation which involves both abnormal vascular morphology and disordered growth of a whole lung. The major group within this definition is the scimitar syndrome, which we choose to mean a hypoplastic lung with anomalous venous drainage and various degrees of collateral arterial supply. Nine typical cases of scimitar are presented, with three closely related cases. Six other cases of dysmorphic lungs are also present. The relationships between the groups are discussed, and an effort is made to clarify the nomenclature used in this condition.