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Epidural anaesthesia and Familial Dysautonomia (the Riley Day syndrome). Three case reports

1998; Wiley; Volume: 8; Issue: 1 Linguagem: Inglês

10.1046/j.1460-9592.1998.00674.x

1460-9592

J. Challands, Evan E Facer,

Genetic Neurodegenerative Diseases

Epidural anaesthesia in Familial Dysautonomia (FD) or the Riley Day syndrome has not previously been reported. Three children with FD presenting for redo Nissen fundoplication were managed with epidural anaesthesia. Cases 1 and 2 had had their original Nissen fundoplication without epidural anaesthesia. In Case 3, FD had not yet been diagnosed when she had her first operation, and it was performed with epidural anaesthesia. The anaesthetic management of these cases with and without epidural anaesthesia is described and discussed.