Congenital pulmonary capillary hemangiomatosis: Report of two cases and review of the literature
2003; Wiley; Volume: 36; Issue: 3 Linguagem: Inglês
10.1002/ppul.10245
ISSN8755-6863
AutoresAngélica Oviedo, Lisa P. Abramson, Ross Worthington, John Dainauskas, Susan E. Crawford,
Tópico(s)Vascular anomalies and interventions
ResumoAbstract Pulmonary capillary hemangiomatosis (PCH) is a rare disease characterized by pulmonary hypertension and excessive neovascularization within the pulmonary interstitium, vasculature, and airways. We describe two unusual cases of congenital PCH. Both cases had concurrent anomalies, including renal and urinary bladder agenesis and hypertropic cardiomyopathy. In one case, capillary proliferation caused significant impingement of the proximal bronchial airways. A review of the current literature is described. Pediatr Pulmonol. 2003; 36:253–256. © 2003 Wiley‐Liss, Inc.
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