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Sézary syndrome in an 11-year-old girl

1993; Elsevier BV; Volume: 28; Issue: 1 Linguagem: Inglês

10.1016/0190-9622(93)70017-n

1097-6787

Lynn Meister, Ana M. Duarte, Joanna A. Davis, Jorge Luís Estepa Pérez, Lawrence A. Schachner,

Lymphoma Diagnosis and Treatment

All forms of cutaneous T-cell lymphoma are rare in children. We describe an 11-year-old girl who had generalized exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, mycosis cells in the skin and lymph nodes, and Sézary cells in the peripheral blood. Results of a biopsy specimen of involved skin showed changes consistent with mycosis fungoides. A classic case of Sézary syndrome has not previously been reported in childhood or preadolescence. All forms of cutaneous T-cell lymphoma are rare in children. We describe an 11-year-old girl who had generalized exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, mycosis cells in the skin and lymph nodes, and Sézary cells in the peripheral blood. Results of a biopsy specimen of involved skin showed changes consistent with mycosis fungoides. A classic case of Sézary syndrome has not previously been reported in childhood or preadolescence.