Artigo Acesso aberto Revisado por pares

A Naturally Occurring Human Minidysferlin Protein Repairs Sarcolemmal Lesions in a Mouse Model of Dysferlinopathy

2010; American Association for the Advancement of Science; Volume: 2; Issue: 50 Linguagem: Inglês

10.1126/scitranslmed.3000951

ISSN

1946-6242

Autores

Martin Krahn, Nicolas Wein, Marc Bartoli, William Lostal, Sébastien Courrier, Nathalie Bourg-Alibert, Karine Nguyen, Christophe Vial, Nathalie Streichenberger, Véronique Labelle, D. Depétris, Christophe Pécheux, France Leturcq, Pierre Cau, Isabelle Richard, Nicolas Lévy,

Tópico(s)

RNA regulation and disease

Resumo

A naturally occurring miniversion of the dysferlin protein found in a patient shows that gene therapy by minigene transfer may be possible in dysferlinopathies.

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