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Mitochondrial dysfunction in amyotrophic lateral sclerosis also affects skeletal muscle

2006; Wiley; Volume: 34; Issue: 2 Linguagem: Inglês

10.1002/mus.20566

1097-4598

Luc Dupuis, José‐Luis González de Aguilar, Andoni Echaniz‐Laguna, Jean‐Philippe Loeffler,

Muscle Physiology and Disorders

Muscle & NerveVolume 34, Issue 2 p. 253-254 Letters to the Editor Mitochondrial dysfunction in amyotrophic lateral sclerosis also affects skeletal muscle Luc Dupuis PhD, Luc Dupuis PhD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this authorJose-Luis Gonzalez de Aguilar PhD, Jose-Luis Gonzalez de Aguilar PhD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this authorAndoni Echaniz-Laguna MD, Andoni Echaniz-Laguna MD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this authorJean-Philippe Loeffler PhD, Jean-Philippe Loeffler PhD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this author Luc Dupuis PhD, Luc Dupuis PhD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this authorJose-Luis Gonzalez de Aguilar PhD, Jose-Luis Gonzalez de Aguilar PhD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this authorAndoni Echaniz-Laguna MD, Andoni Echaniz-Laguna MD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this authorJean-Philippe Loeffler PhD, Jean-Philippe Loeffler PhD Laboratoire de Signalisations Moléculaires et Neurodégénérescence INSERM U-692, Univerité Louis Pasteur, Faculté de Médecine, 11 rue Humann, 67085 Strasbourg, FranceSearch for more papers by this author First published: 26 April 2006 https://doi.org/10.1002/mus.20566Citations: 10Read the full textAboutPDF ToolsRequest permissionExport citationAdd to favoritesTrack citation ShareShare Give accessShare full text accessShare full-text accessPlease review our Terms and Conditions of Use and check box below to share full-text version of article.I have read and accept the Wiley Online Library Terms and Conditions of UseShareable LinkUse the link below to share a full-text version of this article with your friends and colleagues. Learn more.Copy URL Share a linkShare onEmailFacebookTwitterLinkedInRedditWechat No abstract is available for this article. References 1 Clement AM, Nguyen MD, Roberts EA, Garcia ML, Boillee S, Rule M, et al. Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice. Science 2003; 302: 113–117. 2 Derave W, Van Den Bosch L, Lemmens G, Eijnde BO, Robberecht W, Hespel P. Skeletal muscle properties in a transgenic mouse model for amyotrophic lateral sclerosis: effects of creatine treatment. Neurobiol Dis 2003; 13: 264–272. 3 Desport JC, Preux PM, Magy L, Boirie Y, Vallat JM, Beaufrere B, et al. Factors correlated with hypermetabolism in patients with amyotrophic lateral sclerosis. Am J Clin Nutr 2001; 74: 328–334. 4 Dobrowolny G, Giacinti C, Pelosi L, Nicoletti C, Winn N, Barberi L, et al. Muscle expression of a local Igf-1 isoform protects motor neurons in an ALS mouse model. 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