Congenital protein C deficiency and superior sagittal sinus thrombosis causing isolated intracranial hypertension.
1994; BMJ; Volume: 57; Issue: 5 Linguagem: Inglês
10.1136/jnnp.57.5.655
ISSN1468-330X
AutoresC Confavreux, Pascal Brunet, P. Petiot, M. Berruyer, M Trillet, G Aimard,
Tópico(s)Venous Thromboembolism Diagnosis and Management
ResumoThe first case of a superior sagittal sinus thrombosis causing isolated intracranial hypertension as a result of congenital protein C deficiency is reported. Such a possibility must not be overlooked. Anticoagulation is recommended as a treatment for cerebral venous thrombosis. In the case of congenital protein C deficiency, vitamin K antagonists must be started cautiously due to the risk of skin necrosis.
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