Portal de Periódicos da CAPES

Neurocutaneous melanosis presenting with intracranial amelanotic melanoma.

1999; National Institutes of Health; Volume: 20; Issue: 3 Linguagem: Inglês

Bart Vanzieleghem, Marc Lemmerling, Rudy N. Van Coster,

Vascular Tumors and Angiosarcomas

We describe imaging findings in a 2-year-old girl with neurocutaneous melanosis and malignant cerebral melanoma. Because the cerebral melanoma in this child was of the amelanotic type, high-signal intensity on unenhanced T1-weighted images was not present. The cutaneous lesions played a crucial role in establishing a correct (presumed) histopathologic diagnosis on the basis of the imaging findings. To our knowledge this is the first report describing an intracranial amelanotic malignant melanoma in association with neurocutaneous melanosis.