Artigo Acesso aberto Revisado por pares

Measurements of Plasma Methoxytyramine, Normetanephrine, and Metanephrine as Discriminators of Different Hereditary Forms of Pheochromocytoma

2011; American Association for Clinical Chemistry; Volume: 57; Issue: 3 Linguagem: Inglês

10.1373/clinchem.2010.153320

ISSN

1530-8561

Autores

Graeme Eisenhofer, Jacques W.M. Lenders, Henri Timmers, Massimo Mannelli, Stefan K. Grebe, Lorenz C. Hofbauer, Stefan R. Bornstein, Oliver Tiebel, Karen T. Adams, Gennady Bratslavsky, W. Marston Linehan, Karel Pacák,

Tópico(s)

Pituitary Gland Disorders and Treatments

Resumo

Pheochromocytomas are rare catecholamine-producing tumors derived in more than 30% of cases from mutations in 9 tumor-susceptibility genes identified to date, including von Hippel-Lindau tumor suppressor (VHL); succinate dehydrogenase complex, subunit B, iron sulfur (Ip) (SDHB); and succinate dehydrogenase complex, subunit D, integral membrane protein (SDHD). Testing of multiple genes is often undertaken at considerable expense before a mutation is detected. This study assessed whether measurements of plasma metanephrine, normetanephrine, and methoxytyramine, the O-methylated metabolites of catecholamines, might help to distinguish different hereditary forms of the tumor.

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