Hepatic Telangiectases and Portosystemic Encephalopathy in Osler-Weber-Rendu Disease
1968; Elsevier BV; Volume: 54; Issue: 5 Linguagem: Inglês
10.1016/s0016-5085(68)80167-2
ISSN1528-0012
AutoresDan Michaeli, Isaac Ben‐Bassat, Hylton I. Miller, Victor Deutsch,
Tópico(s)Neurological Complications and Syndromes
ResumoSummary A patient suffering from hereditary hemorrhagic telangiectases presented with an epigastric bruit and experienced, for 6 months prior to her death, repeated episodes of portosystemic encephalopathy. Angiography demonstrated tremendous dilation of the hepatic arteries and extensive portacaval shunting of blood through telangiectatic channels in the liver parenchyma. The latter were confirmed by biopsy and, later, at autopsy, which also revealed the absence of hepatic scarring. The occurrence of portosystemic encephalopathy due to hepatic telangiectases represents a new aspect of Osler-Weber-Rendu disease.
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