Current Status of Hyperammonemic Syndromes
1982; Lippincott Williams & Wilkins; Volume: 2; Issue: 4 Linguagem: Inglês
10.1002/hep.1840020417
ISSN1527-3350
AutoresDavid B. Flannery, Edward Y. Hsia, Barry Wolf,
Tópico(s)Pediatric Hepatobiliary Diseases and Treatments
ResumoHepatologyVolume 2, Issue 4 p. 495S-506S ArticleFree Access Current Status of Hyperammonemic Syndromes† David B. Flannery, David B. Flannery Departments of Human Genetics and Pediatrics, Children's Medical Center, Medical College of Virginia, Richmond, Virginia 23298 and Departments of Genetics and Pediatrics, John A. Burns School of Medicine, University of Hawaii at Manoa, Honolulu, Hawaii 96826Search for more papers by this authorY. Edward Hsia, Y. Edward Hsia Departments of Human Genetics and Pediatrics, Children's Medical Center, Medical College of Virginia, Richmond, Virginia 23298 and Departments of Genetics and Pediatrics, John A. Burns School of Medicine, University of Hawaii at Manoa, Honolulu, Hawaii 96826Search for more papers by this authorBarry Wolf, Corresponding Author Barry Wolf Departments of Human Genetics and Pediatrics, Children's Medical Center, Medical College of Virginia, Richmond, Virginia 23298 and Departments of Genetics and Pediatrics, John A. Burns School of Medicine, University of Hawaii at Manoa, Honolulu, Hawaii 96826 Dr. Wolf is the recipient of NIH Research Career Development Award AM 00677.Barry Wolf, M.D., Ph.D., Department of Human Genetics, Medical College of Virginia, P.O. Box 33, MCV Station, Richmond, Virginia 23298.===Search for more papers by this author David B. Flannery, David B. Flannery Departments of Human Genetics and Pediatrics, Children's Medical Center, Medical College of Virginia, Richmond, Virginia 23298 and Departments of Genetics and Pediatrics, John A. Burns School of Medicine, University of Hawaii at Manoa, Honolulu, Hawaii 96826Search for more papers by this authorY. Edward Hsia, Y. Edward Hsia Departments of Human Genetics and Pediatrics, Children's Medical Center, Medical College of Virginia, Richmond, Virginia 23298 and Departments of Genetics and Pediatrics, John A. Burns School of Medicine, University of Hawaii at Manoa, Honolulu, Hawaii 96826Search for more papers by this authorBarry Wolf, Corresponding Author Barry Wolf Departments of Human Genetics and Pediatrics, Children's Medical Center, Medical College of Virginia, Richmond, Virginia 23298 and Departments of Genetics and Pediatrics, John A. Burns School of Medicine, University of Hawaii at Manoa, Honolulu, Hawaii 96826 Dr. Wolf is the recipient of NIH Research Career Development Award AM 00677.Barry Wolf, M.D., Ph.D., Department of Human Genetics, Medical College of Virginia, P.O. Box 33, MCV Station, Richmond, Virginia 23298.===Search for more papers by this author First published: July/August 1982 https://doi.org/10.1002/hep.1840020417Citations: 61 † This article is No. 156 from the Department of Human Genetics at the Medical College of Virginia, Richmond, Virginia. AboutPDF ToolsRequest permissionExport citationAdd to favoritesTrack citation ShareShare Give accessShare full text accessShare full-text accessPlease review our Terms and Conditions of Use and check box below to share full-text version of article.I have read and accept the Wiley Online Library Terms and Conditions of UseShareable LinkUse the link below to share a full-text version of this article with your friends and colleagues. Learn more.Copy URL Share a linkShare onFacebookTwitterLinkedInRedditWechat References 1 Lowenstein JM. Ammonia production in muscle and other tissues: the purine nucleotide cycle. Physiol Rev 1972; 52. 382– 414. 2 Krebs HA, Hems R, Lund P. Some regulatory mechanisms in the synthesis of urea in mammalian liver. Adv Enzyme Regul 1973; 11: 361– 377. 3 Hsia YE. Inherited hyperammonemic syndromes. Gastroenterology 1974; 67: 347– 374. 4 S Grisolia, R Baguena, F Major (eds.). In: The urea cycle. New York: J. 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