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Desmoplastic fibroma of bone. A report of six cases

1984; British Editorial Society of Bone & Joint Surgery; Volume: 66-B; Issue: 2 Linguagem: Inglês

10.1302/0301-620x.66b2.6707066

2044-5377

Francesco Bertoni, P Calderoni, Patrizia Bacchini, Mario Campanacci,

Sarcoma Diagnosis and Treatment

The clinical and pathological features of six cases of desmoplastic fibroma of bone are presented. Desmoplastic fibroma is rarely seen as a primary tumour of bone; when it does occur the sites of predilection are the long bones, but other sites such as the scapula and os calcis can be involved. Radiographically the lesion tends to expand the bone from within; it is well-demarcated and lytic, often with a trabeculated soap-bubble appearance. The cellular structure and the morphological arrangement are similar to those of aggressive fibromatosis of soft tissues. Differential diagnosis from malignant spindle-cell lesions of bone is important because the treatment of choice for desmoplastic fibroma of bone is simply excision with a thin layer of healthy tissue.