ENETS Consensus Guidelines Update for the Management of Patients with Functional Pancreatic Neuroendocrine Tumors and Non-Functional Pancreatic Neuroendocrine Tumors
2016; Karger Publishers; Volume: 103; Issue: 2 Linguagem: Inglês
10.1159/000443171
ISSN1423-0194
AutoresMassimo Falconi, Barbro Eriksson, Gregory Kaltsas, Detlef K. Bartsch, Jaume Capdevila, Martyn Caplin, Beata Kos‐Kudła, Dik J. Kwekkeboom, Guido Rindi, Günter Klöppel, Nicholas S. Reed, Réza Kianmanesh, Robert T. Jensen,
Tópico(s)Lung Cancer Research Studies
Resumobe considered in three groups: the more frequent gastrinomas and insulinomas considered independently and all the rare F-P-NETs (RFTs) considered together and as a separate category (Appendix 1 and table 1 ).Most P-NETs occur as sporadic tumors (non-inherited), although a variable proportion of the different F-P-NETs occurs as part of an inherited syndrome.MEN1 remains the most important inherited condition responsible for 20-30% of gastrinomas and <5% of insulinomas or RFTs [4][5][6][7] ; and uncommon causes of inherited P-NETs include von Hippel Lindau disease (VHL), von Recklinghausen's syndrome (neurofibromatosis 1) and tuberous sclerosis [4,5] .In each of the latter inherited
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