Rapunzel syndrome
2001; Elsevier BV; Volume: 358; Issue: 9290 Linguagem: Inglês
10.1016/s0140-6736(01)06410-8
ISSN1474-547X
Autores Tópico(s)Hernia repair and management
ResumoA 4-year-old girl of normal intelligence presented with an 18-month history of worsening epigastric pain, partly alleviated by antacids. This pain awakened her at night. Gastric endoscopy showed a large trichobezoar. The bezoar was removed surgically and was cast in the shape of the stomach, extending via strands to further bezoars in the third part of the duodenum and proximal jejunum. She acknowledged hair twisting, pulling, and chewing and was persuaded to desist after surgery. Trichobezoars result from trichotillomania in healthy children and in children with syndromes such as Prader Willi syndrome. They may cause complete small intestinal obstruction and perforation. The constellation of small intestinal obstruction by trichobezoar is known as Rapunzel syndrome, after the German princess in Grimms' fairytales who let her golden hair down from her tower to facilitate a tryst with her lover.
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