Artigo Revisado por pares

Critical Coronary Artery Stenosis and Aortitis in a Patient with Relapsing Polychondritis

2008; The Journal of Rheumatology Publishing Company Limited; Volume: 35; Issue: 9 Linguagem: Inglês

ISSN

1499-2752

Autores

Jonathan D Stein, Peter Lee, Bindee Kuriya, J Tenenbaum, Lorretta B. Daniel, Jagdish Butany, Yves Provost, T. David,

Tópico(s)

Vascular Anomalies and Treatments

Resumo

To the Editors: Relapsing polychondritis (RP) is a multisystem autoimmune disease with cartilage inflammation. Cardiovascular manifestations are associated with significant morbidity and mortality1,2. Vasculitis involving the coronary arteries is rare. Our patient developed severe ostial lesions in 2 major coronary arteries and aortitis requiring surgical intervention despite intensive medical treatment. A 30-year-old male Caucasian dental surgeon developed a painful, swollen left ear in January 2001. He was otherwise asymptomatic. Initial laboratory investigations were normal. A clinical diagnosis of relapsing polychondritis was made. His ear inflammation resolved after prednisone 30 mg daily for 3 weeks. Over the next 5 years he…

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