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The Mayer-Rokitansky Syndrome: Pathogenesis, Classification and Management

1986; Lippincott Williams & Wilkins; Volume: 136; Issue: 3 Linguagem: Inglês

10.1016/s0022-5347(17)45004-x

1527-3792

William F. Tarry, John W. Duckett, F. Douglas Stephens,

Urological Disorders and Treatments

No AccessJournal of Urology1 Sep 1986The Mayer-Rokitansky Syndrome: Pathogenesis, Classification and Management W.F. Tarry, John W. Duckett, and F. Douglas Stephens W.F. TarryW.F. Tarry , John W. DuckettJohn W. Duckett , and F. Douglas StephensF. Douglas Stephens View All Author Informationhttps://doi.org/10.1016/S0022-5347(17)45004-XAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissionsReprints ShareFacebookLinked InTwitterEmail Agenesis of the vagina in karyotypic female subjects may be accompanied by other defects of the urogenital system. We describe 8 cases that exemplify nearly all variants in the group of müllerian and renal anomalies that we identify as the Mayer-Rokitansky syndrome. We trace the association of system defects to errors of formation of the wolffian body. This structure is the progenitor of the gonad and wolffian duct, which although temporary in the female subject, gives rise to the ureter and is the path finder of the müllerian system. Errors of formation or premature atrophy of the wolffian duct, or intrinsic müllerian organizers lead to the array of anomalies in this syndrome. Vaginal agenesis was found to be associated with müllerian, renal or ovarian defects in numerous embryological combinations. We propose a müllerian classification, and describe the current diagnostic modalities and techniques of surgery. © 1986 by The American Urological Association Education and Research, Inc.FiguresReferencesRelatedDetailsCited byFlack C, Barraza M and Stevens P (2018) Vaginoplasty: Combination Therapy Using Labia Minora Flaps and Lucite Dilators—Preliminary ReportJournal of Urology, VOL. 150, NO. 2 Part 2, (654-656), Online publication date: 1-Aug-1993.Stephens F (2018) Editorial CommentJournal of Urology, VOL. 140, NO. 5 Part 1, (937-937), Online publication date: 1-Nov-1988. Volume 136Issue 3September 1986Page: 648-652 Advertisement Copyright & Permissions© 1986 by The American Urological Association Education and Research, Inc.MetricsAuthor Information W.F. Tarry More articles by this author John W. Duckett More articles by this author F. Douglas Stephens More articles by this author Expand All Advertisement PDF downloadLoading ...