Portal de Periódicos da CAPES

Artigo Acesso aberto Produção Nacional Revisado por pares

BIBTEX RIS

Ewing's Sarcoma Family Tumors in the Jaws: Case Report, Immunohistochemical Analysis and Literature Review

2017; Stanford University Highwire Press; Volume: 31; Issue: 3 Linguagem: Inglês

10.21873/invivo.11087

1791-7549

Ana Regina Casaroto, Marcelo Bonifácio da Silva Sampiéri, Cléverson Teixeira Soares, Paulo Sérgio da Silva Santos, Renato Yassutaka Faria Yaedú, José Humberto Damante, Vanessa Soares Lara,

Management of metastatic bone disease

Due to the low incidence of the Ewing9s Sarcoma (ES) family tumors, the available epidemiology is likely to be unreliable, and at present, there are no standard diagnostic or clinical guidelines outlining their management. This report describes a case of peripheral primitive neuroectodermal tumor (ES/pPNET) which initially mimicked cystic lesions, and describes a comparison between ES and ES/pPNET in the jaws by the World Health Organization classification. This review addressed 63 cases published in the English literature between 1950 and 2016. The majority of cases were ES. Both ES and ES/pPNET mimicked other benign entities such as traumatic, cystic and inflammatory lesions. The patients who died of their disease had a history of metastatic tumors, and primary tumor located in the mandible and maxilla for ES and ES/pPNET, respectively. The differentiation of the ES family tumors from other small blue-cell tumors may be difficult and requires familiarity with histological and immunohistochemical features.