Artigo Revisado por pares

CRANIOFACIAL FIBROUS DYSPLASIA INVOLVING THE ZYGOMATIC BONE AND ORBIT

2017; Elsevier BV; Volume: 124; Issue: 2 Linguagem: Inglês

10.1016/j.oooo.2017.05.227

ISSN

2212-4411

Autores

Patrícia Guerra Peixe Gonçalves, ANDRÉIA FERREIRA DO CARMO, HUGO COSTA NETO, Luiz Carlos Alves Júnior, Adriano Rocha Germano, Bruno César de Vasconcelos Gurgel, Hébel Cavalcanti Galvão,

Tópico(s)

Bone health and treatments

Resumo

Fibrous dysplasia (FD) is a benign slowly progressive disease in which normal craniofacial bones are replaced by immature fibro-osseous tissue. It may involve any part or combination of the skeleton, ranging from an asymptomatic monostotic lesion, to severe polyostotic disease. Herein we present a 27-year-old male patient with extensive maxillary FD, involving adjacent bones. Extraoral clinical examination revealed a lesion involving zygomatic bone and orbit, with a hardened consistency and mucosa-colored, causing effacement of nasolabial folds, labial and nasal wing displacement. Intraoral clinical examination revealed swelling in the oral vestibule, with dental displacement and vital teeth without mobility signals. The lesion was present from birth, showing growth spurt at age 16. An incisional biopsy was performed and the histopathologic diagnosis was FD. Clinical, radiographic and histopathologic findings are essential to confirm the lesion. There are many options of treatment available, but still management of FD remains challenging, especially in extensive lesions.

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